Abstract
A 70-year-old man was seen at the hospital because of abdominal distension. He was diagnosed as having a psedomyxoma peritonei and subsequently operated on. During the operation, the intraperitoneal cavity was found to contain a large amount of gelatinous material, with a total weight of 6,100 g. The origin of the pseudomyxoma peritonei proved to be a ruptured urachal cyst. The urachal cyst and the dome of the urinary bladder were excised. We removed as much of the gelatinous material as possible and intraperitoneal lavage with 5% glucose was performed. Then 100 mg of cisplatin was infused into the peritoneal cavity. On histological examination, the urachal cyst was identified as an invasive well-differentiated mucinous adenocarcinoma. The term “pseudomyxoma peritonei” is used to describe an unusual clinical condition characterized by the massive amounts of gelatinous mucinous ascites, associated with a mucinous tumor, disseminated on the peritoneal surfaces and the omentum. The appendix or ovary are the most common sites of origin, and other primary sites have been rarely reported. Since pseudomyxoma peritonei arising from the urachus is extremely rare, we have reported this case with a review of the literature.