Abstract
We report a rare case of a clear cell tumor of the lung. Recent data suggest that it is patristic in origin, and it has been proposed that it should be considered as one of the families of PEComas-neoplasms that originate from perivascular epithelioid cells. A 65-year-old woman, was found to have a round, abnormal shadow in the left upper lung at the time of rectal cancer surgery. After the rectal cancer surgery, a partial resection of the left lung was performed. On histopathology, the tumor cells were found to have abundant and clear cytoplasm containing glycogen and were supported by sinusoid-like vessels. Furthermore, the tumor was positive for PAS and HMB-45. Based on these findings, the tumor was diagnosed as a clear cell tumor of the lung.