Abstract
We present a case of leiomyosarcoma of the inferior vena cava (IVC). A 35-year-old woman was admitted to the hospital because leg edema and proteinuria. A large right adrenal tumor, which occupied the right lobe of liver and the IVC was detected by means of computed tomography and abdominal ultrasonography, so she was transferred to our hospital for treatment. After percutaneous transhepatic portal embolization, we performed a partial resection of the inferior vena cava including the tumor, a right liver lobectomy, and a right adrenalectomy. The IVC was reconstructed using a Gore Tex Graft (ringed, 20 mm in diameter). Immunohistochemical staining of the tumor tissue revealed that αSMA and caldesmon were expressed in the tumor cells, and s100, CD34 and CD56 were not expressed. The pathological diagnosis was leiomyosarcoma originating from the IVC. Although postoperative adjunctive therapy was not performed, the patient has been well without recurrence for 2 years and 6 months after the surgery.