Abstract
A 64-year-old woman underwent resection of a congenital choledochal cyst and flow-diversion surgery 13 years earlier, and the pathological diagnosis showed no evidence of malignancy. Following the primary surgery, a yearly routine CT scan showed a mass located at a hilar bile duct, which was diagnosed as hilar bile duct cancer. Right hepatectomy and reconstruction of the bile duct were performed, and R0 resection was achieved. The resected tumor was pathologically diagnosed as papillary adenocarcinoma of the hilar bile duct. Currently, 6 months after the second surgery, the patient is doing well without any signs of recurrence. The current case suggests the necessity of long-term postoperative observation after flow-diversion surgery for congenital choledochal cyst.
