Abstract
A 50-year-old female visited our hospital because of an abdominal mass detected at a medical checkup. She was affected with tuberous sclerosis. Contrast enhanced CT scan revealed a 10-cm retroperitoneal tumor with fatty density at the dorsal aspect of the ascending colon. We performed laparotomy and found a retroperitoneal angiomyolipoma. Renal angiomyolipoma is the major comorbidity of tuberous sclerosis, and in this case there were findings of renal angiomyolipoma as well. However, extrarenal angiomyolipoma rarely occurs in tuberous sclerosis patients. Retroperitoneal angiomyolipoma has been reported in 32 cases to date. This is the first case report of retroperitoneal angiomyolipoma associated with tuberous sclerosis.
