A Case of Incomplete-type Carney's Triad for which LECS was Performed for Residual Stomach GIST

Abstract

The case was a 23-year-old female patient. At the age of 18, she visited our hospital with the chief complaint of dizziness and sense of fatigue. Anemia was noted. An endoscopic examination of her upper gastrointestinal tract revealed multi-nodular gastrointestinal stromal tumor (GIST), and owing to its extensive lesion, we performed a laparoscopic distal gastrectomy. During the follow-up period, at the age of 22, she was found to have a 10-mm nodule in the lingular segment of the left lung, for which we conducted thoracoscopic partial lung resection. The pathological diagnosis was a lung chondromatous hamartoma. Six months later, an endoscopic examination of the upper gastrointestinal tract showed a 15-mm submucosal tumor at the residual side of the lesser curvature, and biopsy of the mucosal incision yielded a pathological diagnosis of GIST. When the patient's age was 23, we performed a laparoscopic and endoscopic cooperative surgery of gastric partial resection and preserved the residual stomach. The present case was a rare case of incomplete-type Carney's triad of gastric GIST complicated with lung chondromatous hamartoma, having features different from those of ordinary, adult-type gastric GIST. We report our case, together with other 11 cases published in Japan, and a review of the literature.