Abstract
The patient was a 64-year-old man who underwent cholecystectomy at the age of 5 and resection of an extrahepatic bile duct with choledochojejunostomy at the age of 19 for congenital biliary dilatation. He developed hepatitis B at the age of 38 and had subsequently been followed in our hospital. His carbohydrate antigen 19-9 level was slightly elevated in September 2016 and markedly elevated in December 2016. Abdominal contrast-enhanced computed tomography (CT) scan showed intrahepatic cholangiocarcinoma in the S2 region, a duodenal adenoma, and a huge intestinal sac. We performed left hemi-hepatectomy and resected the duodenal adenoma and the intestinal sac. The pathological diagnosis was intrahepatic cholangiocarcinoma. Postoperatively, he had bile leakage that we treated with drainage. In a review of the literature, this case is of resectable intrahepatic cholangiocarcinoma arising after the longest interval following the excision of congenital biliary dilatation. We report this rare case and review the literature.
