Abstract
[Objective] The purpose of this study was to evaluate the postnatal management of prenatally diagnosed congenital cystic adenomatoid malformation (CCAM), an abnormality of lung development.
[Methods] We retrospectively assessed the medical records of 10 cases prenatally diagnosed with CCAM.
[Results] The mean gestational week at diagnosis was 22.6±3.0 weeks, the mean birth weight was 2,861±411 g and the mean gestational age at delivery was 37.2±2.7 weeks. Of the 10 patients, two were symptomatic in the neonatal period. One of them died before surgery and the remaining one underwent surgery during the neonatal period. Eight were asymptomatic at birth. One of them underwent surgery during the neonatal period because of a potential risk of developing early respiratory symptoms. The remaining seven were discharged without surgery. Four of them underwent elective surgery at a later date. Lobectomy was performed in all cases operated upon. There was no significant difference in the rate of perioperative complications between neonatal surgery and elective surgery cases.
[Conclusion] Neonatal surgery for CCAM should be considered in symptomatic patients and those who are at risk of developing respiratory symptoms. The timing of elective surgery in the post-neonatal period should be considered on a case-by-case basis, depending on the condition of the patient. Early surgery should be considered in symptomatic CCAM patients. If CT shows a persisting lesion for more than 6 months, elective surgery should be planned even in asymptomatic cases.
