A Case Report of Primary Buttock Angiosarcoma with Lung and Liver Metastases with a Dismal Prognosis

Abstract

Angiosarcomas tend to occur in the head and neck region, and those on the trunk are associated with better convalescence. A case of hemangiosarcoma appearing in multiple organs and showing rapid development is presented. The patient was a 78-year-old woman diagnosed with a hemangioma. After resection of a buttock tumor, computed tomography showed a nodular lesion in the lower lobe of the right lung. A partial lung resection was therefore performed. The relationship of this lesion to the buttock tumor was unclear. One year later, computed tomography identified a growing tumor in her right hepatic lobe. A right hepatic lobe resection was necessary, but due to insufficient residual liver capacity, a right portal vein ligation and tumor biopsy were performed. The pathology was hemangiosarcoma due to metastases from the skin and lung lesions. A right hepatic lobectomy was attempted ; however, she developed hemorrhagic shock on the 19th postoperative day. Computed tomography showed growth of the liver tumor and intratumoral hemorrhage. She died 56 days after surgery as a result of disseminated intravascular coagulation (DIC). An autopsy showed multiple hemangiosarcomas throughout her liver. Her cause of death was determined to be liver failure and DIC associated with Kasabach-Merritt syndrome.