2010 Volume 30 Issue 7 Pages 1043-1049
Ehlers-Danlos syndrome is a disease caused by connective tissue disorders. The clinical features of Ehlers-Danlos syndrome are hyperextensibility of the skin, propensity to bruise and bleed, and hyperextension of the joints. Recently we experienced perioperative management of a patient with Ehlers-Danlos syndrome.
The patient was a 49-year-old woman who had been clinically diagnosed with Ehlers-Danlos syndrome in childhood. The patient underwent an emergent operation for recurrent right obturator hernia under general anesthesia. During the perioperative management, we encountered several problems, which were subcutaneous extravasation of intravenous fluids and muscle relaxant, prediction of difficult airway management, hypertension due to surgical stress during the operation, and severe postoperative joint pain, and the formation of new subcutaneous bleeding.
In the perioperative management of the patient with Ehlers-Danlos syndrome, avoiding complications that arise due to their tissue fragility and hemorrhage is very important.
