Abstract
Tuberous sclerosis is a neuroectodermal disease marked by a classic triad of adenoma sebaceum, epilepsy, and mental retardation. This disease poses serious problems during anesthesia, but there has been little discussion of it in the literature. We used an intraoperative electroencephalogram monitor during anesthesia in a patient with epilepsy due to tuberous sclerosis.
A 5-year-old boy with tuberous sclerosis was scheduled for ophthalmologic and plastic surgery under general anesthesia. He had epilepsy, mental retardation, adenoma sebaceum and paroxysmal supraventricular tachycardia. In spite of anti-convulsant therapy, he was subject to some attacks of epilepsy everyday. To avoid the epileptic drug action of euflurane, anesthesia was induced and maintained not by enflurane but by oxygen-nitrous oxide-isoflurane. His electroencephalogram was taken with a Life ScanTM (NeurometricsTM) prior to anesthetic induction. He did not show any abnormal signs in the central nervous system and the surgery was performed without any complications. Isoflurane may be an appropriate anesthetic for patients with epilepsy.
