Abstract
We anesthetized a 23-year-old male with Noonan syndrome and hypertrophic cardiomyopathy (HCM) three times for a scoliosis operation. Patients with Noonan syndrome have facial, cardiovascular, and skeletal abnormalities, which should be properly evaluated pre-operatively. Each time, anesthesia was induced with fentanyl and midazolam, and was maintained with nitrous oxide, 0.5-1% isoflurane and fentanyl. Radial artery and pulmonary artery catheters were used for hemodynamic monitoring and for maintenance of appropriate hemodynamics for HCM. It is necessary in patients with HCM to avoid tachycardia and maintain preload and afterload during anesthesia.
