Abstract
A 67-year-old female with oculopharyngodistal myopathy (OPDM) underwent plastic surgery for ptosis. There have been no reports on the anesthetic management of OPDM, while there have been various reported cases concerning sensitivity to intravenous anesthetics and muscle relaxants in oculopharyngeal dystrophy and ocular myopathy as resemblance diseases. Anesthesia was therefore induced and maintained with oxygen, nitrous oxide and sevoflurane, and the trachea was intubated without muscle relaxants. In conclusion, VIMA was a useful anesthetic technique for patients with OPDM.