Congenital External Nasal Mass with Incomplete Midline Cleft Lip and Midline Upper Lip Sinus of the Philtrum: A Case Report

Abstract

　　The accessory auricle often occurs in front of the tragus, but it may occur on the posterior surface of the auricle, cheek, or neck. There are multiple case reports of skin masses similar to the accessory auricle in the nostrils, but few studies have reported such masses at the tip of the nose. We report a rare case of accessory auricle and an accessory auricle-like skin mass on the external nose with facial abnormalities such as incomplete midline cleft lip and midline upper lip sinus of the philtrum.
　　Our case may be described as Pai syndrome; however, there is no consensus on diagnostic criteria and the etiology was unknown. Thus, the present case suggests that multiple morphological abnormalities may appear at the same time in a single place or in multiple places. Further research on etiology and embryology is necessary.