Abstract
Although an increasing number of congenital cholesteatoma cases have been reported recently, bilateral congenital cholesteatoma is still rare, with only 15 cases reported in the international literature. We encountered a case of bilateral congenital cholesteatoma. A 6-year-old boy was referred to our hospital by a local otolaryngologist because of a white mass of the left tympanic membrane. The right tympanic membrane seemed to be normal, but computed tomography revealed a soft-tissue dense mass in the right middle ear cavity with extension medial to the body of the incus. A type w.o. modified tympanoplasty was performed on the left ear and six months later, a type III-c modified tympanoplasty was performed on the right ear.