Abstract
Tumors in the lacrimal sac are relatively rare, and 70% of them are malignant. The patient often visits the department of ophthalmology because symptoms are similar to chronic dacryocystitis. We report a case of a 79-year-old female with a malignant tumor in the lacrimal sac. She received tumor resection with orbital exenteration, removal of a part of the maxilla, parotidectomy and neck dissection. The pathological study revealed that the tumor is primary adenocarcinoma of the lacrimal sac, which has the same characteristics as salivary duct carcinoma. Otolaryngologists should treat patients with tumors of the lacrimal sac because an extended operation is required in case of advanced cancer.