Abstract
A case of nasal chondromesenchymal hamartoma (NCMH) with severe orbital deviation in infant is reported. The tumor involved the nasal cavity, ethmoid sinus and floor of the anterior cranial fossa. A 2-year-old male was presented with swelling of the external nose and buccal region, epistaxis, nasal obstruction and severe orbital deviation to upper-lateral direction. He visited our department in February 2001. Magnetic resonance images (MRI) demonstrated a mass in the left nasal cavity, involving the ethmoid sinus and floor of the anterior cranial fossa, and compressing the left orbit with mild exophthlmos. Computed tomography (CT) revealed calcified capsule. An excisional biopsy specimen suggested NCMH. An anterior craniof acial resection using bi-coronal skin incision and hemi-facial dismasking approach was performed, and the tumor was almost totally extirpated except in a small area around the exposed optic nerve. The tumor extended into the ethmoid sinus, sphenoid sinus and orbit. However, nasal septum and anterior skull base were not invaded. The histological examination of the extirpated specimen revealed a final diagnosis of NCMH without malignancy. The patient is free from recurrence of the tumor or ophthalmologic complication 1 year after the operation.
