A Case of Orthognathic Surgery for NBCIE

Abstract

Non-bullous congenital ichthyosiform erythroderma （NBCIE） includes hereditary dermatosis caused by dyskeratosis along with hyperkeratosis and erythema. A 22-year-old woman with NCBIE was treated with orthognathic surgery under general anesthesia. Deliberate perioperative considerations are needed before anesthesia equipment can be attached to the skin and the body temperature of such patients must be appropriately managed. A normal body temperature was maintained throughout the procedure and no perioperative complications developed. We concluded that a concomitant forced-air warming system with an underbody blanket help to maintain the body temperature of patients with NCBIE during general anesthesia. Silicon tape is also useful for fixing tracheal tubes and intravenous catheters in place when patients with NCBIE undergo surgical procedures.