Abstract
A case of newborn female infant with omphalocele and Prune belly Syndrome was reported. She was born at full term: the delivery was spontaneous from a cephalic presentation. Her birth weight was 2,820 g. There was no family history of anomalies. In the lower abdominal region, there were two large bulging areas lacking covering skin. The upper one was an omphalocele measuring 5cm in diameter. The another bulging was an exstrophied bladder. One stage repair of the abdominal wall and the bladder could be performed. After the operation, we noticed that the abdominal wall was flaccid and thin. CT scaner of the abdomen showed absence of musculture of the abdominal wall and left hydronephrosis. Drip Infusion Pyelography showed left non-visualizing kidney. The post operative course has been satisfactory, but carefull follow up of renal function and grouth is mandatory.
