Abstract
Distal ureteral atresia (DUA) is rarely found with a megaureter. Two cases with distal ureteral atresia were reported with the review of 20 cases collected from literature. The first patient was a 1 year and 7 months old boy and the second was a 1 year and 7 months old girl. In both patients, an abdominal mass was found by a pediatrician when they were brought because of high fever or diarrhea. A large retroperitoneal cyst which occupied in the area between the kidney and the bladder was found by CT and US. The first patient was operated on with a preoperative diagnosis of retroperitoneal cyst. A diagnosis of distal ureteral atresia was made, however, preoperatively in the second patient. In literature only 2 cases were diagnosed correctly before operation. Symptoms and signs suggest DUA; 1) abdominal distension from infancy, 2) recurrent febrile episodes without pyuria, 3) abdominal mass, 4) abdominal pain. IVP shows that either renal pelvis is not visualized or displaced caudally and laterally. CT and US show a retoroperitoneal cyst involving the area between the kidney to the bladder. These clinical features and laboratory findings would be helpful to make a correct diagnosis of DUA preoperatively.
