Abstract
Two cases of Menkes' kinky hair disease having urologic complications were herein reported. The first case was diagnosed Menkes' kinky hair disease at 6-month old. He noted multiple bladder diverticula, right vesicoureteral reflux and right hydronephrosis at 4-year-9-manth old. The cause of these urologic complications was thought to be a consequence of an increasing disturbance in innervation of the bladder. The other case performed the left nephrectomy at 26-day old at birth, because of massive bleeding from left kidney. He was diagnosed Menkes' kinky hair disease at three months after the operation. The cause of bleeding was thought to be the characteristic disorder of vessels which frequently noticed on the Menkes' kinky hair disease. To authors' knowlege, as this renal complication of Menkes' kinky hair disease, it has not been reported in the literature.
