Abstract
Congenital superior mesenteric arteriovenous malformation is rare lesion. Our review of the literature revealed only two cases, a 31-year-old male and a 40-year-old male. A male infant, weighing 2,480 gr, was born at 37 weeks and 6 days by vaginal delivery after uncomplicated pregnancy. He developed the disseminated intravascular coagulation syndrome soon after birth and treated with exchange transfusion. He was transferred to our hospital for abdominal tumor at fourth day of his life. A diagnosis of congenital superior mesenteric arteriovenous malformation was made by abdominal CT scan and aortography. This is the first reported case of this disease seen in newborn infant.
