Abstract
This paper describes clinical characteristics of malignant rhabdoid tumor of the kidney(MATK) from our experiences and the literatures. In two infants experienced in our institute, the MRTK were found in association with brain tumors, one of which was cerebellar medulloblastoma and the other was metastatic MRTK. Both patients died of rapid growth of the brain tumors. For the last 15 years, only ten of infantile malignant renal tumors(MRTK or neonatal Wilms') had been reported in Japan. Among them, all of MRTK(five cases) had expired within one or eight months postoperatively. Associated brain tumors were found in three of five MRTK in this series. Since the rapid appearance of local recurrences or multiple metastases of the tumor is seen, additional extensive studis in attempt to develop the effective treatment for these highly malignant renal tumors are necessary.