Abstract
A case of herniation of the appendix, which formed an appendiceal-umbilical fistula, into the umbilical cord was reported. Herniation of the appendix into the umbilical cord is ex- tremely rare and only a few cases have been reported. According to these reports, its etiology remains unknown but two possibilies are suggested: 1) Accidental herniation of the appendix through the weak umbilical ring. 2) Persistent vitelline duct, which connects the appendix with the umbilical ring.