Abstract
The authors reported a case of malignant rhabdoid tumor of the left kidney. The case was a 3-year and 11-month-old boy, who had a 9 × 15 cm sized tumor in the left retroperitoneal space. The tumor showed no invasive extension, and was successfully exstirpated along with the left kidney and the regional and para-aortic lymphnodes. Metastatic legions in the paraaortic lymphnodes were proved histologically. Therefore, the patient was classified into stageIII MRTK After the radical operation, regimen DD of the NWTS-4 (ACD + VCR + ADR + Radiation) was continued for 15 months without any signs of the disease. Prognosis of this disease is poor, because of the relapse which frequently occurs within 4 months after operation and the majority of the patients dies within 1 year. Seven among 47 suvivors accumulated in the literatures were clinically reviewed in this report.
