Abstract
Bronchopulmonary foregut malformation (BFM) is a rare form of sequestration of the lungs. We have experienced 3 cases of BFM during the past 10 years. Case 1; A male newborn baby was transfered to our hospital because of esophageal atresia. He had a respiratory distress syndrome and showed cyanosis. A chest roentgenogram demonstrated complete opacification of the right hemithorax. A division of tracheoesophageal fistula and a esophagoesophagostomy had been performed on the same day. Postoperative esophagogram showed a large esophagobronchial fistula. Total lung sequestration with BFM was diagnosed at the second operation. Abnormal blood supply was not certified, and pneumonectomy was carried out. Subsequently, aortopexy was performed because of left bronchial stenosis 3 months after the second surgery. Case 2; A premature female baby was admitted to our institution because of herelip, cleft palate, and anorectal malformation. Esophageal atresia, malformation of the intestine, and annular pancreas were also seen in this patient. An esophagogram demonstrated an esophagobronchial fistula extending from the lower esophagus to the right lower opaque field of the lung. A left intralobar sequestration with a fistula was removed at the operation. Case 3; At autopsy of a 7-day-old boy with congenital jejunal atresia, total sequestration of the right lung in communication with the lower esophogus was disclosed. He had VSD in addition.
