A Case of Extraskeletal Myxoid Chondrosarcoma in a Child

Abstract

This is a case of a 10-year-old boy with an extraskeletal myxoid chondrosarcoma. A solid and painless mass was discovered in the subject's left shoulder region. A local excision was performed and histological examination revealed that it was an extraskeletal myxoid chondrosarcoma. Two weeks later, a wide excision was performed, and subsequently chemotherapy was applied for three months. The child has been doing well, with no evidence of recurrence, ten months after the second excision. Extraskeletal Myxoid Chondrosarcoma is a rare tumor that usually appears in the soft tissue of the extremities. In children, this tumor is extremely rare, and only nine cases have been reported to date. In general, extraskeletal myxoid chondrosarcoma has been considered to be only slightly aggressive. Of these nine children, however, six died of the disease within several months after the diagnosis. Seemingly this tumor is more aggressive in children than in adults. It, therefore, requires a careful treatment coupled with close observation and a long-term follow-up.