Ebstein's Anomaly : Clinical Study of 23 Patients.

Abstract

Between 1961 and June, 1989, 23 patients with Ebstein's anomaly were evaluated at Sapporo Medical College. Three patients were followed without surgery and two of them died with congestive heart failure at 9 months and at 10 years after the follow up. Eleven patients had four different types of palliative operations (Glenn in 5, Blalock-Taussing in 2, Brock in 3, and closure of the intra atrial communication in 4). Two patients had Hardy's plication. But none of these 11 patients with palliative operations and two patients after Hardy's operation survived for long-term periods. Twelve patients had tricuspid valve replacement with one operative and three late deaths. Eight patients were followed ranging from 6 months to 24 years (mean 11years). Six of the eight survivors were in NYHA class I, and two were in class II. Clinical results of valve replacement for Ebstein's anomaly were satisfactory, and it provided excellent long-term results.