Abstract
A case of complete duplication of the extrahepatic bile duct in a 13-year-old boy is reported. The patient suffered severe epigastric pain with hyperamylasemia, which was thought to be due to a possibly abnormal arrangement of the pancreatico-biliary ductal junction. Preoperative diagnosis of the lesion was made successfully by endoscopic retrograde cholangio-pancrea-ticography, revealing two ducts separated throughout their length, but draining together through a papilla. Resection of the duplicated choledochus and hepaticojejunostomy relieved the symptoms. Fifty-seven patients, including 12 children, with such duplication of the biliary system were reviewed, and the clinical characteristics, diagnoses, and surgical treatments for this condition are discussed.