Congenital cystic adenomatoid malformation with prenatal ultrasound examination successfully treated with lower lobe resection, before presenting progressive respiratory distress

Abstract

Prenatal detection of serial sonographic study makes it possible to diagnose a baby with congenital cystic adenomatoid malformation (CCAM) before manifesting respiratory distress. A full term infant was admitted to our hospital maternal transport and planned delivery. The sonographic study had prenatally revealed a macrocystic tumor in the left pleural cavity with polyhydroamnios. Prompt management including CT scanning and surgical treatment was successfully done. CT scanning revealed a large mass containing innumerable small cysts, mainly involving S_6. A right lower lobectomy was performed at 3 hours after delivery. The infant was discharged on the 11th postoperative day. The pathological findings confirmed the diagnosis of CCAM. Fetuses with CCAM have a good clinical prognosis with maternal transport, planned delivery, and immediatal surdery.