Abstract
Congenital ureteral valves are so rare that up to the end of 1994, only 35 cases have been reported in Japan, including 14 pediatric cases. We encountered a 14-year-old male patient with an ureteral valve. He had left flank pain as his chief complaint. His preoperative diagnosis was left hydronephrosis resulting from stenosis of the ureleropelvic junction. During subsequent surgery, we confirmed a diaphragmatic ureteral valve having a pinpoint opening in the center of the lesion, and removed it. Most cases of this disease reported in the literature have been diagnosed during surgery or at postmortem examinations. However, there are recent reports suing that it was diagnosed preoperatively and that the treament was conducted non-invasively by using the endoscopic method. Keeping in mind that this disease can be a factor associated with disturbances of the upper urinary passage, it is important to attempt to diagnose this disease before surgery.
