Abstract
We report a rare association of congenital pyloric atresia and diaphragmatic eventration. A 2, 506-g girl was born at 38 weeks and six days of gestation without a history of hydramnios. On the day of birth she began vomiting, and seven days after birth she was admitted to our hospital. A plain radiograph of the chest and the abdomen showed a dilatated stomach bubble partially protruding into the left thoracic cavity and no gas beyond the pylorus. A contrast study revealed an obstruction in the pyloric region. On the eighth day we performed a laparotomy. A median part of the left diaphragm protruded 30×25 mm in size into the thoracic cavity and was diagnosed as partial diaphragmatic eventration. In order to repair the diaphragm, we performed a plication. The pylorus showed a membranous obstruction, and we performed an excision of the membrane and pyloroplasty according to the Heineke-Mikulicz method. One day after the operation the tracheal tube was removed. On the fifth postoperative day, oral feeding was started. Congenital pyloric atresia is a rare malformation. To our knowledge congenital pyloric atresia associated with diaphragmatic eventration has not been described in the literature.
