Choledochal Cyst and Duodenal Atresia : A Rare Combination of Malformations

Abstract

A rare case of congenital duodenal atresia (DA) associated with a choledochal cyst (CC) is reported. After birth, the patient was admitted to another hospital where she received the diagnosis of duodenal atresia. She underwent duodenoduodenostomy for correction of type III duodenal atresia associated with an annular pancreas. She recovered uneventfully after the operation and did well for 8 years. Eight years after the initial operation, she underwent a thorough health examination. Abdominal ultrasonography demonstrated a CC and dilated intrahepatic bile ducts. Magnetic resonance cholangiopancreatography showed an anomalous arrangement of the choledochus and the main pancreatic duct. A diffusely dilated extrahepatic bile duct was resected, and a hepaticoduodenostomy was performed after a cholecystectomy. The patient was discharged without complications.