Abstract
An 8-year-old boy was referred to our hospital for treatment of the ileus. He was refractory to conservative therapy and an emergent operation was done. Strangulation was the cause of the ileus and it was released. Apart from the obstruction, we found an elastic hard tumor in the ileum. It was well circumscribed, and 2cm in diameter. Partial resection of the ileum was performed. Histopathological examination revealed that it was a 15×8mm subserosal tumor with prominent eosinophilic infiltration. Immunohistochemically, the lesion was positive for CD1a and S-100. We finally diagnosed it as Langerhans cell histiocytosis (LCH). The post-operative course was uneventful and he was discharged on POD 7. Further examination revealed no other lesions, so we finally diagnosed it as the single organ-single site type. As far as we know, this was the first case diagnosed as the SS type of LCH by immunohistochemical examination. The prognosis of multiple organ-multiple site LCH involving the digestive tract is very poor, so a detailed whole body retrieval is necessary.
