Abstract
The patient was born at 37 weeks' gestation after an ultrasound scan at 19 weeks' gestation revealed a possible right-sided abdominal cyst compressing the right diaphragm with hydramnion. MRI at 30 weeks' gestation showed the same findings described above. Passage of a nasogastric tube was unsuccessful after birth. Chest-abdominal x-rays revealed opacification of the right partial hemithorax and large gastric duodenal bubbles with no distal bowel gas. On day 0 of life, duodenoduodenostomy, gastrostomy, and duodenostomy were performed for esophageal atresia and duodenal atresia. In the laparotomy, there was an extremely dilated second portion of the duodenum with distal membranous atresia, and oral side stenosis. On day 24 of age, the esophageal atresia was repaired and hypoplastic lung and elevated right diaphragm were identified. Postoperative bronchofiberscopy showed aplasia of the right middle-lower bronchus. The combined anomalies of pulmonary hypoplasia with esophageal atresia and duodenal atresia are extremely rare. Only 4 cases have been reported in the English literature.
