Abstract
A case of intestinal malrotation with spontaneous pneumoperitoneum was reported. A 6-day-old male infant was born at 38 weeks gestation with a birth weight of 2,506 g. He was admitted to our medical center because of vomiting, and pneumoperitoneum was noted on X-ray and CT scans. Laparotomy revealed no gastrointestinal tract perforation, however intestinal malrotation was found. Ladds procedure was performed and the postoperative course was uneventful. A case of intestinal malrotation with pneumoperitoneum is rare, and it is suspected that pneumoperitoneum seems to have been induced by intestinal malrotation.