Abstract
We herein report a case of liver vascular anomalies indistinguishable from presurgical malignant tumors. A seven-year-old male visited our hospital for Lowe Syndrome. Abdominal ultrasonography, and examination results revealed a mass in the right hepatic lobe. Small nodes were detected around the tumor by enhanced computed tomography scanning. Although the margin of tumor was clearly enhanced, the central lesion was not. Enhanced MRI showed low intensity lesions on T1-weighted images and high intensity lesions on T2-weighted images. We therefore suspected hemangioendothelioma, although malignant tumors, such as undifferentiated sarcoma, were not ruled out. We finally decided to remove all the tumors via right hepatic lobectomy. Histopathological examinations of the resected specimen revealed congenital hemangioma or capillary malformation, which was subsequently classified as vascular malformations. In pediatric liver tumors, it is sometimes difficult to make the correct diagnosis based only on imaging or blood tests. Especially in hypervascular tumors, a biopsy may be misleading, and therefore a surgical resection should be considered in treating such cases.
