Abstract
There are few long-term survivors of chronic idiopathic intestinal pseudo-obstruction (CIIP). Here, we report the case of a 20-year-old man with CIIP. He was born after 37 weeks of gestation and was hospitalized in the neonatal intensive care unit (NICU) owing to low birth weight. His bowel condition was normal at first; however, he developed strangulation ileus at two months of age and underwent partial resection of the intestine following ileostomy. After the stoma closure, he started to exhibit the episode that repeat ileus symptoms. He was referred to our hospital at the age of nine, and he has been receiving nutrition parenterally. The excretion of bowel contents from the ileal stoma was insufficient, and bowel decompression using a long tube was also unsuccessful. At the age of 14, the right side of the colon and a major part of the small intestine were removed, leaving 70 cm of the oral jejunum; then, side-to-side jejunocolostomy with end-jejunostomy was performed. After the operation, his general condition improved markedly with efficient drainage from the ileus tube and jejunostomy. From our limited experience, shortening of the intestine might be an effective surgical strategy in CIIP patients for the adequate drainage of intestinal content and the prevention of TPN-related complications.
