Abstract
Most cases of odontogenic tumors occur as intraosseos odontoma, and extraosseous odontoma is rarely observed. In this report, we describe a unique case of extraosseous odontoma. A male neonate, 13 days after birth, was examined owing to a tumor on the right side of the oral cavity as the primary symptom. A pedunculated elastic hard tumor of 20 mm diameter was recognized. Ultrasonographic findings showed a round low-echoic tumor with calcification. CT scans showed a protruding tumor of 15 × 10 × 17 mm size without intracranial extension. Upon diagnosis of epignatus, total excision was performed under general anesthesia 3 months after birth. The pathologic diagnosis was extraosseous odontoma. The postoperative course was uneventful. Although extraosseous odontoma is extremely rare, it is important to consider it as a differential diagnosis.