2016 Volume 52 Issue 5 Pages 1051-1055
A 6-year-old boy diagnosed with WAGR syndrome presented with bloody urine and a left abdominal tumor. On ultrasonographic examination, a mass (maximum 10 cm) was observed in the left kidney. The mass was diagnosed as Wilms tumor and tumorectomy was planned. However, the boy presented with fever, and infectious endocarditis was strongly suspected owing to his previous history of heart operation with an Amplatzer device. Instead of the postponement of the tumorectomy, preoperative chemotherapy (ActD + VCR for four weeks) was initiated. On post-chemotherapeutic day 20, the boy suffered from severe anemia, and multiple intratumoral hemorrhages were observed on contrast-enhanced CT images. Therefore, an emergency tumorectomy was performed. We herein describe our experience with a difficult case of Wilms tumor treated as an oncologic emergency.
