2017 Volume 53 Issue 7 Pages 1264-1268
Rhabdomyosarcoma (RMS), a soft tissue sarcoma, is one of the most common pediatric cancers. Although it normally arises within the head and neck regions and the genitourinary system, primary RMS of the ovary is extremely rare. In this report, we present the case of a 9-year-old patient with an embryonal RMS arising in the left ovary. She complained of progressive abdominal pain and constipation for the past 2 months. As the pain rapidly progressed, causing anorexia, she was brought to our hospital. Physical examination revealed a lower quadrant abdominal mass. Computed tomography showed a large heterogenous pelvic mass and some ascetic fluid. Tumor biopsy was performed and histopathological analysis indicated embryonal RMS. She received chemotherapy including vincristine, doxorubicin, cyclophosphamide, ifosfamide, and cisplatin with good response to the chemotherapy. After 7 months of hospitalization, surgical resection was performed, and a mass in the left ovary was discovered. Her primary tumor was completely resected, and she received postoperative chemotherapy. No recurrence of the disease was seen in a follow-up period of approximately 45 months at the time of writing this report.
