Double Common Bile Duct With Pancreaticobiliary Maljunction Diagnosed Preoperatively: A Case Report

Abstract

Double common bile duct is an extremely rare anomaly, in which 2 common bile ducts exist. We encountered a case of a 2-year-old girl with double common bile duct associated with pancreaticobiliary maljunction, which was diagnosed preoperatively. Firstly, she complained of abdominal pain with vomiting and presented with hyperamylasemia. She was transferred to our hospital with the diagnosis of choledochal cyst. MRCP and DIC-CT revealed double common bile duct associated with atypical pancreaticobiliary maljunction. Intraoperative cholangiography was carried out to confirm the details of the anatomy of the extrahepatic bile duct. The accessory common bile duct branched from the right hepatic duct and joined the main pancreatic duct. We performed a diversion surgery via resection of the extrahepatic bile duct, including the accessory common bile duct. The postoperative course was satisfactory. Careful preoperative imaging tests enabled safe operation with an appropriate margin for extrahepatic bile duct resection.