2018 Volume 54 Issue 7 Pages 1379-1383
A male infant weighing 3,188 g and diagnosed prenatally as having omphalocele was delivered by an emergency cesarean section performed at 35 weeks of gestation. In addition, he had the characteristic facial features, muscle tone reduction, coat-hanger-like rib morphology, and a small thorax. As there was no hernial rupture, abdominal wall closure was performed on day 10 after birth. There was a strong adhesion in the hernial sac and the ileocecum, and the ileum was injured. An ileal stoma was constructed in the umbilicus, and a purse-string skin closure was performed during stoma closure on day 34 after birth. The postoperative umbilical appearance was satisfactory. After surgery, he was diagnosed as having the Kagami-Ogata syndrome. Umbilical stoma requires umbilicoplasty during stoma closure. This procedure is easy and can be quickly performed, helps reduce surgical invasion, and results in excellent tolerability. Therefore, it is effective for cases with underlying diseases, such as in the case presented, and it can be applied to general umbilical stoma closure.