2019 Volume 55 Issue 4 Pages 850-853
We report a case of a 12-year-old girl with sialoblastoma of the submandibular gland. She had a mass of 2 × 2 cm size in the left-sided submandibular since birth. The mass did not grow. We diagnosed the swelling lymph node by clinical examination. She and her family wanted the tumor to be removed, and we completely removed it under general anesthesia. Histopathologically, the tumor was diagnosed as sialoblastoma. Sialoblastoma is an extremely rare congenital salivary gland tumor with malignancy. In the literature, we found 50 cases of sialoblastoma, although this case is the first report in Japan. No recurrence was observed one year after the tumor resection.