A Case of Multilocular Cystic Nephroma With Elevated Serum CA19-9

Abstract

Multilocular cystic nephroma (MLCN) has been described as a benign renal tumor. However, imaging modalities, such as CT, MRI, and US, cannot differentiate MLCN from a subset of cystic renal cell carcinomas. Therefore, the majority of MLCN cases are treated by radical nephrectomy. We report a case of MLCN surgically treated. A 13-month-old girl presented with hematuria, which was diagnosed as MLCN with ureterocele on the basis of abdominal CT findings, and her serum CA19-9 level was high. We performed total nephrectomy. Histopathological analysis showed no malignancy. However, the CA19-9 level in the cyst was substantially high.