2021 Volume 57 Issue 1 Pages 33-37
We herein report a case of congenital duodenal atresia associated with biliary atresia. A male infant prenatally diagnosed as having congenital duodenal atresia by fetal ultrasound scan was born by cesarean section at 34 weeks and two days of gestation, and duodeno-duodenostomy was performed one day after birth. The postoperative course was uneventful; however, white stools were observed from the age of about forty days. Intraoperative cholangiography revealed that there was a cyst near the junction of the cystic and common hepatic ducts, and when contrast cholangiography was performed directly from the cyst, the left and right hepatic ducts emerged, but the lower common bile duct to the duodenum was not observed. Therefore, we diagnosed him as having biliary atresia (I-cyst), and he underwent extrahepatic obstructive bile duct resection and hepaticojejunostomy. Although there are few reports of biliary atresia associated with congenital duodenal atresia, of those reports, most patients presented with anastomotic biliary atresia in which the lower common bile duct is closed or narrowed. There may be some common mechanisms shared by both biliary obstruction and duodenal atresia.
