2021 Volume 57 Issue 3 Pages 639-644
An 11-year-old girl who suffered from fever, abdominal pain, and the presence of a sudden upper abdominal mass was referred to our institution. After several examinations, the diagnosis of a large intraabdominal lymphangioma with intrahepatic bile duct dilatation was suspected, and it was located in the ligamentum hepatoduodenale. Since conservative treatment did not reduce the lesion size, percutaneous cyst drainage was performed on the third day of hospitalization. A CT examination after achieving a reduction in the lesion size revealed a liver cyst. Laparoscopic fenestration was performed seven days after admission. A vessel-sealing system was used to open the cyst wall to prevent any postoperative bleeding and bile leakage. She was discharged on the fifth postoperative day without any complications and has been doing well for three months after the operation without any recurrence. If a malignant tumor can be ruled out for a pediatric giant liver cyst, then it is desirable to perform preoperative drainage in order to make an accurate diagnosis, provide symptom relief, and thereafter perform surgery.