2021 Volume 57 Issue 5 Pages 878-883
A 13-year-old girl who presented with left lower abdominal pain was referred to our hospital. Enhanced abdominal CT revealed a 130 mm tumor in the pelvis invading the left ureter and the left iliac artery and vein. We performed laparoscopic-assisted biopsy, and on the basis of biopsy findings, we diagnosed the patient as having rhabdomyosarcoma. We performed radical resection because we confirmed that the tumor had shrank after chemoradiotherapy. We resected the tumor together with the left ureter and the left iliac artery and vein, and we reconstructed the left common iliac artery using an artificial graft and anastomosed the left ureter to the right ureter (transureteroureterostomy). The patient was administered surgical adjuvant chemotherapy, and she is now healthy at 3 years and 3 months after the surgery with no sign of recurrence. We experienced treating a case of retroperitoneal primary rhabdomyosarcoma invading the left ureter and left iliac artery and vein with a good prognosis by multidisciplinary treatment. The cooperation with specialists of each department seems to provide a safe and useful treatment, even for rhabdomyosarcoma requiring the resection of a combination of major blood vessels and ureters.