2021 Volume 57 Issue 7 Pages 1084-1088
A 7-year-old girl was referred to our hospital because of acute onset and intermittent abdominal pain with an abdominal mass demonstrated by CT scan. Abdominal palpation revealed a mass in the right-lower quadrant and tenderness all over the abdomen without muscular defense. A contrast-enhanced CT scan demonstrated a 10 × 7 × 9 cm solid right-sided mass that was most likely an ovarian tumor. A suspected hematoma in the tumor and the presence of a massive ascites strongly suggested tumor rupture. An emergency laparotomy was performed, and the ruptured right ovarian tumor was found macroscopically without the invasion upon the uterus and uterine tube and thus the enucleation was carried out. The pathological diagnosis was a poorly differentiated Sertoli-Leydig cell tumor (SLCT) of the ovary with a large amount of rhabdomyosarcomatous component (FIGO stage-IC3). She received chemotherapy, radiotherapy and peripheral blood stem cell transplantation, and there has been no evidence of recurrence for four years by now. The pathology showed poor prognosis, and the dissemination of the tumor cells into the abdominal cavity was apparent in our patient and thus a watchful follow-up is mandatory.
