2023 Volume 59 Issue 7 Pages 1088-1094
The patient was a 21-year-old female who had the Potts procedure performed at three months of age for low-type anorectal malformations. She had no history of attendance at our hospital after the age of eight years and had been self-managed since then. She was suffering from constipation one month prior to her arrival at our hospital and was hospitalized the day before by her previous physician. After admission, she developed fecal intestinal obstruction, abdominal compartment syndrome, and ischemia of the lower limbs, and was brought to our hospital for emergency care. Under general anesthesia, an emergency manual decompression was performed, and 9 kg of fecal matter was evacuated. The patient required a long period of intensive care, but she recovered without sequelae and is currently undergoing defecation control with medication and enemas at the Adult Clinic. Long-term follow-up is necessary after anorectal malformation surgery because of the possibility of defecatory dysfunction, abnormalities of the urinary system, spinal cord abnormalities, and sexual dysfunction. Therefore, it is essential to educate patients and their families to understand the disease, consider the treatment plan, and make the transition to adult medical care.
